Search on: ACID, METHYLMALONIC 
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Descriptor English:   Methylmalonic Acid 
Descriptor Spanish:   Ácido Metilmalónico 
Descriptor Portuguese:   Ácido Metilmalônico 
Synonyms English:   Acid, Methylmalonic  
Tree Number:   D02.241.081.337.540.500
Definition English:   A malonic acid derivative which is a vital intermediate in the metabolism of fat and protein. Abnormalities in methylmalonic acid metabolism lead to methylmalonic aciduria. This metabolic disease is attributed to a block in the enzymatic conversion of methylmalonyl CoA to succinyl CoA. 
Indexing Annotation English:   /biosyn /physiol permitted
History Note English:   91(75); was see under MALONATES 1975-90 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AG agonists AA analogs & derivatives
AN analysis AI antagonists & inhibitors
BL blood CF cerebrospinal fluid
CS chemical synthesis CH chemistry
CL classification EC economics
HI history IM immunology
IP isolation & purification ME metabolism
PK pharmacokinetics PD pharmacology
PO poisoning RE radiation effects
ST standards SD supply & distribution
TU therapeutic use TO toxicity
UR urine  
Record Number:   8951 
Unique Identifier:   D008764 

Occurrence in VHL:
 

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